肾上腺表皮样囊肿一例
2021-08-04张南陈英敏
张南,陈英敏
患者女,56岁,因“体检发现左侧肾上腺占位1个月余”入河北省人民医院,无明显临床症状。查体:一般状况良好。
影像表现:超声示左肾后方可探及一低回声团,大小约4.4 cm×4.0 cm×3.4 cm,边界欠清,内回声欠均。彩色多普勒及能量图:左肾后方低回声团未见明显血流信号。MRI示T1WI(图1A)呈高低混杂信号,病变于T1WI反相位较同相位信号未见明显变化(图1B),T2WI呈混杂稍高信号(图1C),扩散加权成像(dif f usion weighted imaging,DWI)呈不均匀高信号(图1D),增强扫描病灶内部强化不明显,包膜可见轻度延迟强化(图1E)。CT示左侧腹膜后区可见团块状稍低密度影(图1F),大小约4.2 cm×3.9 cm×4.0 cm,密度欠均匀,病变内可见散在小点片状脂肪密度影,形态欠规则,局部可见两处类圆形脂肪密度影突起,边缘可见斑点状钙化,病变与左侧肾上腺外侧肢分界欠清,增强扫描未见明显强化(图1G)。

图1 女,56岁,肾上腺表皮样囊肿。A:箭所示为病变部位,MRI平扫T1WI呈高低混杂信号;B:箭所示为病变部位,MRI平扫T1WI反相位较同相位信号未见明显变化;C:箭所示为病变部位,MRI平扫T2WI呈混杂稍高信号;D:箭所示为病变部位,DWI呈不均匀高信号;E:箭所示为病变部位,增强扫描病变内部强化不明显,包膜可见轻度延迟强化;F:箭所示为病变部位,CT平扫呈稍低密度影;G:箭所示为病变部位,CT增强扫描未见明显强化;H:病理图(HE×200)Fig.1 Female,56 years old,epidermoid cyst of the adrenal gland.A:The arrow showsthe lesion,with the mixed signal of high and low on T1 weighted image;B:The arrow shows the lesion,the lesion signal has no obvious change on both in-phase and out-phase sequence;C:The arrow shows the lesion,with the mixed slightly high-signal intensity on T2 weighted image;D:The arrow shows the lesion,DWI shows high signal,and signal is inhomogeneity;E:The arrow shows the lesion,contrast-enhanced scan shows no obvious internal enhancement and slightly delayed enhancement in the capsule;F:The arrow shows the lesion,plain CT scan shows a slightly lower density;G:The arrow shows the lesion,contrast-enhanced CT scan shows no significant enhancement;H:The pathological pictures(HE×200).
影像诊断:考虑来源于左侧肾上腺可能性大,髓样脂肪瘤可能性大。
在腹腔镜下行左侧肾上腺肿瘤切除术,术中见肿物来源于左侧肾上腺,与腔静脉及左肾静脉粘连严重,难以分离,遂切除部分肿瘤。……
